GINGIVAL FIBROMATOSIS WITH HEARING LOSS: A JONES SYNDROME CASE REPORT

Abstract

Introduction: Hereditary Gingival Enlargement (HGF), a rare entity, is also known as familial elephantiasis, elephantiasis gingivae, diffuse fibromatosis. It is a benign, non-haemorrhagic fibrous enlargement of gingival tissue. It is frequently a component feature of many syndromes. Jones syndrome is one such syndrome, characterized by gingival overgrowth and progressive deafness.

Case report: A 27-year-old male patient reported to the Department of Oral Medicine and Radiology with the chief complaint of swollen gums for the past 7 years. The patient also complained of bleeding gums on brushing. The medical history stated a concurrent gradual hearing loss 7 years back. An incisional biopsy was done to confirm the fibrous nature of the diagnosis.

Conclusion: This reporting is of unique case that remained undiagnosed for almost a decade. It also emphasises the need of a multidisciplinary approach during diagnosis and treatment.